MULTIMODAL DIAGNOSTIC APPROACH FOR DETECTION OF A COMBINED CRITICAL CONGENITAL HEART DISEASE IN A NEWBORN OF 1 DAY OLD

 

Khasanova K.A.1,2, Ternovoy S.K. 2,3, Abramyan M.A.1,4, Korochkina E.S.1

 

1 - Morozovskaya Children’s City Clinical Hospital. 2 - Sechenov University 3 - A.L. Myasnikov Institute of Clinical Cardiology. 4 - Peoples' Friendship University of Russia. Moscow, Russia.

 

 

Purpose. Demonstration of modern imaging modalities possibilities in the diagnosis and surgical cor-rection planning of a rare combined congenital heart disease (CHD) in a newborn.

Materials and methods. The article presents a clinical case of patient B., 1 day old, with prenatally suspected complex CHD. Patient was admitted to the intensive care department with signs of de-creased saturation. For surgical management of CHD, the patient underwent trans-thoracic echocar-diography (TTE) and CT-angiography (CTA) of heart and cardiac angiography.

Results. On TTE ductus-dependent CHD, atresia of the pulmonary artery and the absence of in-terventricular and atrial septa were determined. In the preoperative planning the patient underwent a CTA of the heart and cardiac angiography for a detailed assessment of the pulmonary arteries and patent ductus arteriosus (PDA) anatomy. Identifying possible anomalies of the pulmonary veins and aortopulmonary collaterals was important to determine the surgical tactics.

Discussion. TTE has high diagnostic quality in the diagnosis of combined CHD with the pulmo-nary artery atresia, however, it cannot be considered as a final diagnostic step in surgical correction planning due to limitations in the visualization of extracardiac anomalies.

Conclusion. Multimodal diagnostic approach for assessing various anatomical and functional parameters of the heart and extracardiac structures should be used in all children with complex, combined CHD.

 

Keywords: congenital heart defects, CHD, TTE, CTA of the heart, cardiac angiography, pulmo-nary artery atresia, single ventricle, anomalous pulmonary venous return.

 

 

Corresponding author: Khasanova K.A., e-mail: Этот e-mail адрес защищен от спам-ботов, для его просмотра у Вас должен быть включен Javascript

 

For citation: Khasanova K.A., Ternovoy S.K., Abramyan M.A., Korochkina E.S. Multimodal diagnostic approach for detection of a combined critical congenital heart disease in a newborn of 1 day old. REJR 2023; 13(1):134-142. DOI: 10.21569/2222-7415-2023-13-1-134-142.

 

Received: 17.02.23

Accepted: 07.03.23